How to treat early liver beans

summary

The onset of hepatolenticular degeneration was more than that in adolescence, and a few cases could be later than adulthood. The onset age was 4-50 years old. So what are the symptoms of hepatolenticular degeneration?

How to treat early liver beans

First: liver symptoms: Although the patient had accumulated copper in the liver during infancy, liver symptoms rarely occurred before the age of 6. The average age of patients with liver symptoms was about 11 years old. About 80% of the patients developed liver symptoms. In the asymptomatic or early stage of liver cirrhosis, liver function can be normal, or only slightly elevated transaminase, multiple occult disease, showing a chronic course. There are fatigue, anorexia, jaundice, spider nevus, splenomegaly and hypersplenism in the beginning, and eventually lead to portal hypertension, ascites, variceal bleeding and liver failure. Therefore, for patients under 35 years old with HBsAg negative chronic liver disease, we should think of the disease and do laboratory examination to establish the diagnosis. Patients with chronic active hepatitis, a small number of patients with asymptomatic liver, splenomegaly, or transaminase continued to rise without any symptoms.

Second: nervous system symptoms: Patients with this disease, if untreated, will eventually appear liver and nerve damage symptoms. Neurological manifestations usually appear in patients aged 12-30 years old, with an average age of 19 years old. They often develop slowly, with stage remission or aggravation, but also with rapid progress, especially in young patients. The prominent clinical manifestations of nervous system are extrapyramidal symptoms, such as dance like and hand foot movement, dystonia, strange expression, static, intentional or postural tremor, myotonia, bradykinesia, dysarthria, dysphagia, flexion posture and flustered gait. In addition, there may be extensive nerve damage. Such as cortical function damage, performance for progressive mental retardation, inattention, slow thinking, can also have emotional, personality abnormalities, often without reason to cry and laugh, restless, easy to be excited, lack of interest in the surrounding environment, late can have hallucinations and other organic psychiatric symptoms; cerebellar damage, can lead to ataxia and language disorders; cone system damage, tendon hyperreflexes, pathological signs And pseudobulbar paralysis; hypothalamic damage produces obesity, persistent high fever and hypertension. A few patients may have seizures.

Third: mental symptoms: there are at least four aspects of mental disorders: emotional disorders, behavioral disorders, schizophrenia and cognitive impairment. With the above aspects of performance, the treatment is often only partially relieved.

matters needing attention

First of all, we should adjust our diet, eat less food with high copper content, such as animal viscera, fish, shrimp, seafood, nuts and other food with high copper content, which is not suitable for eating. We can eat more food with high zinc content, and we can also take zinc tablets at ordinary times. Secondly, parents should avoid close relatives' marriage. If there are people in the family who have suffered from this disease, it is better to go to the hospital every year for relevant examination, early warning Early diagnosis and treatment. In addition, it is best to carry out testing before preparing for childbirth to prevent the inheritance of the disease.