How many kinds does hematemia have?

summary

Hyperammonemia is a clinical syndrome characterized by abnormal elevation of blood ammonia level and dysfunction of central nervous system. Because of the low incidence rate and the lack of specificity of clinical manifestations, it is easy to cause misdiagnosis and missed diagnosis. Some patients can not get the correct diagnosis until clinical death. How many kinds does hematemia have? Let's talk about it

How many kinds does hematemia have?

Neurotoxicity of hyperammonemia. The severity of clinical symptoms of hereditary hyperammonemia is parallel to the degree of enzyme activity deficiency, that is, the more serious the enzyme deficiency is, the earlier the onset is, the more serious the symptoms are.

During the neonatal period, the symptoms and signs are closely related to brain dysfunction. Usually, the sick baby is normal at birth. After a few days, the symptoms appear after feeding a protein containing diet, such as milk. They are manifested as refeeding, vomiting, shortness of breath, drowsiness, and soon enter deep coma, often with convulsions. Physical examination found that in addition to deep coma, there may be large liver, muscle tension or low.

The symptoms of childhood onset are mostly mild and intermittent. Acute hyperammonemia is manifested as vomiting, neuropsychiatric symptoms, such as ataxia, confusion, anxiety, irritability and aggressive behavior. It can appear drowsiness or even coma, and it can also be manifested as anorexia and headache. The main manifestations of chronic hyperammonemia are progressive brain degeneration, physical dysplasia and mental retardation.

matters needing attention

We should excrete blood ammonia from the body as soon as possible, and give enough heat and essential amino acids to reduce the decomposition of protein in the body. Sufficient liquid and electrolyte were given. Glucose and insulin were added to supplement heat. Fat was infused intravenously, 1g / kg per day.