How does mixed porphyria return a responsibility?

summary

Porphyria, also known as Xuezi treatment, is a group of porphyrin metabolic disorders caused by the lack of certain enzymes or enzyme activity reduction. It can be congenital or acquired. The main clinical symptoms include light sensitivity. This group of diseases mainly include hepatic porphyria, ALA dehydratase deficiency porphyria, acute intermittent porphyria, Hereditary fecal porphyria, variant fecal porphyria, delayed cutaneous porphyria, hepatic erythropoietic porphyria, erythropoietic porphyria, congenital erythropoietic porphyria. X-linked sideroblastic anemia. Let's share my experience with you.

How does mixed porphyria return a responsibility?

Tardive cutaneous porphyria is the most common porphyria, which is caused by the accumulation of urinary porphyrin due to the lack or decreased activity of urinary porphyrinogen decarboxylase. The disease is more common in adult men, more common, more history of liver disease, or drinking history, skin rash is heavy in summer and light in winter. The clinical manifestations were non inflammatory blisters, bullae, erosion, scab and ulcer

Cytogenetic protoporphyria is the second common porphyria, which is caused by the low activity of banding and enzyme and the high level of protoporphyrin IV. it is autosomal dominant inheritance. Erythropoietic protoporphyria is a common disease in children. It is characterized by the pain and burning of the exposed part after the sun exposure.

There will also be erythema edema wheal, severe cases can appear blisters, snow leopard erosion scab, rash repeated attacks, the patient's face was weathered like changes, facial hand back and other exposed parts, visible linear atrophic scars, severe cases can be accompanied by liver disease rash, life-long recurrence.

matters needing attention

First of all, we need to eliminate the possible inducements, including stopping G9 drugs that may aggravate the disease, avoiding sunlight and using sunscreen agents. Delayed type skin porphyria can be treated with hydroxychloroquine and bloodletting if necessary. Erythropoietic protoporphyria.